Sclerodermal kidney crisis, purpose of a case
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Keywords

Acute renal failure, systemic sclerosis, angiotensin converting enzyme inhibitors, hypertension.

How to Cite

1.
Pedroza Pallares Álvaro, Castiglioni T, Bouza G. Sclerodermal kidney crisis, purpose of a case. Rev. Colomb. Nefrol. [Internet]. 2021 Mar. 23 [cited 2022 Aug. 11];8(2):e516. Available from: https://revistanefrologia.org/index.php/rcn/article/view/516

Abstract

Systemic sclerosis (SS), is characterized by the presence of thickening and hardening of the skin (from the Greek "sclero"), it has forms of limited and diffuse manifestation. It is chronic in pattern and manifests with vascular dysfunction and severe systemic connective fibrosis. Sclerodermic renal crisis (CRE) is the severe manifestation in the kidney, and is characterized by:

  • Malignant hypertension, of sudden onset associated with increased plasma renin activity. There is a clinical variant, which presents with normotension, which has a worse prognosis. (UTAH)
  • Acute Renal Failure (ARF).
  • Proteinuria in the non-nephrotic range. Microscopic hematuria and casts are uncommon.

Next, we are going to report the presentation of a case of sclerodermic renal crisis (CRE), in a 60-year-old female patient, who was admitted to our institution with a condition characterized by severe arterial hypertension, severe glomerular filtration drop, microhematuria and proteinuria; which received medical treatment, but due to the persistence of signs and symptoms, it was decided to perform a renal biopsy puncture, which confirmed the diagnosis.

https://doi.org/10.22265/acnef.8.2.516
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References

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Afección renal en la esclerosis sistémica [Internet]. [citado 11 de septiembre de 2020]. Disponible en: https://www.reumatologiaclinica.org/es-pdf-S1699258X06731035

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Copyright (c) 2021 Revista Colombiana de Nefrología

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