Crisis renal esclerodérmica

Pedroza Pallares A, Castiglioni T, Bouza G. Sclerodermic renal crisis. Rev. Colomb. Nefrol. [Internet]. 2022 Jan. 20 [cited 2024 Oct. 8];9(1):e526. Available from: https://revistanefrologia.org/index.php/rcn/article/view/526

Abstract

Systemic sclerosis (SS) is characterized by the presence of thickening and hardening of the skin(from the Greek "sclero"), it has forms of limited and diffuse manifestation. It is chronic in patternand manifests with vascular dysfunction and severe systemic connective brosis. Sclerodermicrenal crisis (CRE) is the severe manifestation in the kidney, and is characterized by: a) Malignanthypertension, of sudden onset associated with increased plasma renin activity. There is a clinicalvariant, which presents with normotension, which has a worse prognosis. (UTAH); b) Acute Renal Fai-lure (ARF); c) Proteinuria in the non- nephrotic range. Microscopic hematuria and casts are uncommon.

Next, we are going to report the presentation of a case of sclerodermic renal crisis (CRE), in a 60-year-old female patient, who was admitted to our institution with a condition characterized by severearterial hypertension, severe glomerular filtration drop, microhematuria and proteinuria; which received medical treatment, but due to the persistence of signs and symptoms, it was decided to perform arenal biopsy puncture, which confirmed the diagnosis.

https://doi.org/10.22265/acnef.9.1.526

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