Hemolytic uremic syndrome atypical after kidney transplantation: a case report and literature review
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Ramírez JI, Gómez ED, Aldana Campos MC, Puerto R, Córdoba JP. Hemolytic uremic syndrome atypical after kidney transplantation: a case report and literature review. Rev. Colomb. Nefrol. [Internet]. 2017 Jan. 1 [cited 2024 Jul. 25];4(1):74-8. Available from: https://revistanefrologia.org/index.php/rcn/article/view/267


Haemolytic uremic syndrome (HUS) is a clinical entity characterized by the appearance of non immune hemolytic anemia, thrombocytopenia and acute renal failure. It is a disease belonging to the group of thrombotic microangiopathy (MAT) which are part of thrombotic thrombocytopenic purpura also (PTT) and some other MAT associated with other medical conditions formerly known as secondary MAT.
Moreover, the variety known as atypical HUS (aHUS) is an ultra-orphan disease that frequently progresses to chronic renal failure (CRF) and is associated with high morbidity and mortality if not properly treated. If a patient presents its first clinical manifestation of aHUS later receive a cadaveric renal transplant which not only makes it an even more exotic case but involves more complexity in their management is presented.

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